- Product Description
- More Information
- Nutrition Facts
Nutrition support of children and adults with maple syrup urine disease (MSUD) or beta-ketothiolase deficiency.
Features:
• Nutrient profile specifically designed for children and adults
• Branched-chain amino acid-free to allow greater intake of intact protein
• Lactose-free, Gluten-free
• Halal
Precautions:
• Not intended as a sole source of nutrition
• Must be supplemented with protein and fluid in prescribed amounts to completely meet isoleucine, leucine, valine and water requirements
• Not for infants under 1 year of age
• Do not heat or use in cooking.
Use under medical supervision.
| Is Rush | Yes |
|---|---|
| Size | Case of 6 |
| Form | Powder |
Ingredients
Corn Syrup Solids, L-Alanine, High Oleic Safflower Oil, Coconut Oil, Sodium Citrate, Soy Oil, L-Proline, L-Lysine Acetate, L-Arginine, Calcium Phosphate, L-Glutamine, Glycine, Magnesium Phosphate, Potassium Chloride, L-Tyrosine. Less than 2% of the Following: L-Serine, L-Phenylalanine, L-Asparagine, L-Threonine, Silicon Dioxide, DATEM, L-Histidine, Potassium Citrate, Potassium Phosphate, L-Methionine, L-Glutamic Acid, L-Cystine Dihydrochloride, L-Tryptophan, L-Aspartic Acid, Calcium Carbonate, Ascorbic Acid, L-Carnitine, Taurine, Choline Chloride, M-Inositol, Ferrous Sulfate, Zinc Sulfate, Niacinamide, dl-Alpha-Tocopheryl Acetate, Calcium Pantothenate, Ascorbyl Palmitate, Mixed Tocopherols, Cupric Sulfate, Manganese Sulfate, Thiamine Chloride Hydrochloride, Riboflavin, Vitamin A Palmitate, Pyridoxine Hydrochloride, Folic Acid, Chromium Chloride, Potassium Iodide, Beta-Carotene, Biotin, Sodium Selenate, Phylloquinone, Sodium Molybdate, Vitamin D3, and Cyanocobalamin.
Serving Size: 100 g Powder
Nutrient Data
| Amount per serving | % Daily Value* | |
|---|---|---|
| Protein Equivalent, g : 30.0 | 30.0 | |
| Fat, g : 14.0 | 14.0 | |
| Carbohydrate, g : 35.0 | 35.0 | |
| Linoleic Acid, mg : 2200 | 2200 | |
| Linolenic Acid, mg : 225 | 225 | |
| L-Carnitine, mg : 200 | 200 | |
| Calories : 410 | 410 |
Vitamins
| Amount per serving | % Daily Value* | |
|---|---|---|
| Vitamin A, IU : 2200 | 2200 | |
| Vitamin A, mcg RE : 660 | 660 | |
| Vitamin D, IU : 300 | 300 | |
| Vitamin D, mcg : 7.5 | 7.5 | |
| Vitamin E, IU : 18 | 18 | |
| Vitamin E, mg alpha-TE : 12.1 | 12.1 | |
| Vitamin K, mcg : 60 | 60 | |
| Thiamin (Vitamin B1), mg : 3.3 | 3.3 | |
| Riboflavin (Vitamin B2), mg : 1.8 | 1.8 | |
| Vitamin B6, mg : 1.3 | 1.3 | |
| Vitamin B12, mcg : 5.0 | 5.0 | |
| Niacin, mg : 16 | 16 | |
| Niacin, mg NE : 21.7 | 21.7 | |
| Folic Acid (Folacin), mcg : 450 | 450 | |
| Pantothenic Acid, mg : 8.0 | 8.0 | |
| Biotin, mcg : 100 | 100 | |
| Vitamin C (Ascorbic Acid), mg : 60 | 60 | |
| Choline, mg : 100 | 100 | |
| Inositol, mg : 70 | 70 |
Minerals
| Amount per serving | % Daily Value* | |
|---|---|---|
| Calcium, mg : 880 | 880 | |
| Phosphorus, mg : 760 | 760 | |
| Magnesium, mg : 225 | 225 | |
| Iron, mg : 13 | 13 | |
| Zinc, mg : 13 | 13 | |
| Manganese, mg : 0.8 | 0.8 | |
| Copper, mg : 1.0 | 1.0 | |
| Iodine, mcg : 100 | 100 | |
| Selenium, mcg : 35 | 35 | |
| Chromium, mcg : 27 | 27 | |
| Molybdenum, mcg : 30 | 30 | |
| Sodium, mg : 880 | 880 | |
| Sodium, mEq : 38.3 | 38.3 | |
| Potassium, mg : 1370 | 1370 | |
| Potassium, mEq : 35.0 | 35.0 | |
| Chloride, mg : 940 | 940 | |
| Chloride, mEq : 26.5 | 26.5 |