Nutrition support of children and adults with a urea cycle disorder, gyrate atrophy of the choroid and retina, or HHH syndrome. Use under medical supervision.
Features:
Precautions:
*Ingredients not genetically engineered.
| Is Rush | Yes |
|---|---|
| Size | 1 Can |
| Form | Powder |
Corn Syrup Solids, High Oleic Safflower Oil, Coconut Oil, Sodium Citrate, Soy Oil, L-Leucine, L-Lysine, Calcium Phosphate, L-Valine, L-Isoleucine, Magnesium Phosphate, Potassium Chloride. Less than 2% of: L-Tyrosine, L-Phenylalanine, L-Threonine, Silicon Dioxide, Modified Corn Starch, Potassium Citrate, Potassium Phosphate, L-Cystine Dihydrochloride, L-Histidine, L-Methionine, Schizochytrium Sp. Oil*, L-Tryptophan, Calcium Citrate, Calcium Carbonate, L-Carnitine, Citric Acid, Ascorbic Acid, Taurine, Choline Chloride, Inositol, Ferrous Sulfate, Zinc Sulfate, Ascorbyl Palmitate, Niacinamide, Calcium Pantothenate, dl-Alpha-Tocopheryl Acetate, Mixed Tocopherols, Copper Sulfate, Thiamine Hydrochloride, Manganese Sulfate, Riboflavin, Pyridoxine Hydrochloride, Vitamin A Palmitate, Folic Acid, Biotin, Chromium Chloride, Potassium Iodide, Sodium Selenate, Phylloquinone, Sodium Molybdate, Vitamin D3, and Vitamin B12.
* Source of DHA.
Serving Size: 100 g Powder
| Amount per serving | % Daily Value* | |
|---|---|---|
| Protein Equivalent, g : 15 | 15 | |
| Fat, g : 17 | 17 | |
| Carbohydrate, g : 45 | 45 | |
| Linoleic Acid, mg : 2800 | 2800 | |
| Linolenic Acid, mg : 275 | 275 | |
| L-Carnitine, mg : 370 | 370 | |
| Calories : 440 | 440 | |
| Potential Renal Solute Load, mOsm : 253 | 253 |
| Amount per serving | % Daily Value* | |
|---|---|---|
| Vitamin A, IU : 1650 | 1650 | |
| Vitamin A, mcg RE : 495 | 495 | |
| Vitamin D, IU : 1100 | 1100 | |
| Vitamin D, mcg : 27.5 | 27.5 | |
| Vitamin E, IU : 13 | 13 | |
| Vitamin E, mg alpha-TE : 7 | 7 | |
| Vitamin K, mcg : 70 | 70 | |
| Thiamin (Vitamin B1), mg : 4 | 4 | |
| Riboflavin (Vitamin B2), mg : 1.8 | 1.8 | |
| Vitamin B6, mg : 1.3 | 1.3 | |
| Vitamin B12, mcg : 7.3 | 7.3 | |
| Niacin, mg : 21 | 21 | |
| Niacin, mg NE : 30.3 | 30.3 | |
| Folic Acid (Folacin), mcg : 510 | 510 | |
| Pantothenic Acid, mg : 10.9 | 10.9 | |
| Biotin, mcg : 140 | 140 | |
| Vitamin C (Ascorbic Acid), mg : 75 | 75 | |
| Choline, mg : 130 | 130 | |
| Inositol, mg : 100 | 100 |
| Amount per serving | % Daily Value* | |
|---|---|---|
| Calcium, mg : 1250 | 1250 | |
| Phosphorus, mg : 1020 | 1020 | |
| Magnesium, mg : 300 | 300 | |
| Iron, mg : 17.0 | 17.0 | |
| Zinc, mg : 17.0 | 17.0 | |
| Manganese, mg : 0.9 | 0.9 | |
| Copper, mg : 2 | 2 | |
| Iodine, mcg : 150 | 150 | |
| Selenium, mcg : 40 | 40 | |
| Chromium, mcg : 37 | 37 | |
| Molybdenum, mcg : 40 | 40 | |
| Sodium, mg : 1175 | 1175 | |
| Sodium, mEq : 51.1 | 51.1 | |
| Potassium, mg : 1800 | 1800 | |
| Potassium, mEq : 46 | 46 | |
| Chloride, mg : 1325 | 1325 | |
| Chloride, mEq : 37.4 | 37.4 |