Nutrition support of children and adults with maple syrup urine disease (MSUD) or beta-ketothiolase deficiency. Use under medical supervision.
Features:
Precautions:
*Ingredients not genetically engineered.
| Is Rush | Yes |
|---|---|
| Size | Case of 6 |
| Form | Powder |
Corn Syrup Solids, L-Alanine, High Oleic Safflower Oil, Coconut Oil, Sodium Citrate, Soy Oil, L-Proline, L-Lysine, L-Arginine, Calcium Phosphate, L-Glutamine, Glycine, Magnesium Phosphate, Potassium Chloride, L-Tyrosine. Less than 2% of: L-Phenylalanine, L-Serine, L-Asparagine, L-Threonine, Silicon Dioxide, Modified Corn Starch, Potassium Citrate, L-Histidine, Potassium Phosphate, L-Methionine, Schizochytrium Sp. Oil*, L-Glutamic Acid, Calcium Citrate, L-Cystine Dihydrochloride, Calcium Carbonate, L-Tryptophan, Citric Acid, L-Aspartic Acid, Ascorbic Acid, L-Carnitine, Taurine, Choline Chloride, Inositol, Ferrous Sulfate, Zinc Sulfate, Ascorbyl Palmitate, Niacinamide, Calcium Pantothenate, dl-Alpha-Tocopheryl Acetate, Mixed Tocopherols, Copper Sulfate, Thiamine Hydrochloride, Manganese Sulfate, Riboflavin, Pyridoxine Hydrochloride, Vitamin A Palmitate, Folic Acid, Biotin, Chromium Chloride, Potassium Iodide, Sodium Selenate, Phylloquinone, Sodium Molybdate, Vitamin D3, and Vitamin B12.
* Source of DHA.
Serving Size: 100 g Powder
| Amount per serving | % Daily Value* | |
|---|---|---|
| Protein Equivalent, g : 30 | 30 | |
| Fat, g : 14 | 14 | |
| Carbohydrate, g : 35 | 35 | |
| Linoleic Acid, mg : 2200 | 2200 | |
| Linolenic Acid, mg : 225 | 225 | |
| L-Carnitine, mg : 200 | 200 | |
| Calories : 410 | 410 | |
| Potential Renal Solute Load, mOsm : 296 | 296 |
| Amount per serving | % Daily Value* | |
|---|---|---|
| Vitamin A, IU : 1500 | 1500 | |
| Vitamin A, mcg RE : 450 | 450 | |
| Vitamin D, IU : 900 | 900 | |
| Vitamin D, mcg : 22.5 | 22.5 | |
| Vitamin E, IU : 12 | 12 | |
| Vitamin E, mg alpha-TE : 5.9 | 5.9 | |
| Vitamin K, mcg : 60 | 60 | |
| Thiamin (Vitamin B1), mg : 3.3 | 3.3 | |
| Riboflavin (Vitamin B2), mg : 1.6 | 1.6 | |
| Vitamin B6, mg : 1.1 | 1.1 | |
| Vitamin B12, mcg : 5 | 5 | |
| Niacin, mg : 16 | 16 | |
| Niacin, mg NE : 21.7 | 21.7 | |
| Folic Acid (Folacin), mcg : 425 | 425 | |
| Pantothenic Acid, mg : 8 | 8 | |
| Biotin, mcg : 100 | 100 | |
| Vitamin C (Ascorbic Acid), mg : 60 | 60 | |
| Choline, mg : 100 | 100 | |
| Inositol, mg : 82 | 82 |
| Amount per serving | % Daily Value* | |
|---|---|---|
| Calcium, mg : 975 | 975 | |
| Phosphorus, mg : 760 | 760 | |
| Magnesium, mg : 225 | 225 | |
| Iron, mg : 13 | 13 | |
| Zinc, mg : 13 | 13 | |
| Manganese, mg : 0.8 | 0.8 | |
| Copper, mg : 1.5 | 1.5 | |
| Iodine, mcg : 100 | 100 | |
| Selenium, mcg : 35 | 35 | |
| Chromium, mcg : 27 | 27 | |
| Molybdenum, mcg : 30 | 30 | |
| Sodium, mg : 880 | 880 | |
| Sodium, mEq : 38.3 | 38.3 | |
| Potassium, mg : 1370 | 1370 | |
| Potassium, mEq : 35 | 35 | |
| Chloride, mg : 940 | 940 | |
| Chloride, mEq : 26.5 | 26.5 |